Erythema Elevatum Diutinum in Association with IgA Monoclonal Gammopathy of Undetermined Significance A Case Report

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Katie
Dr. Shalabi
Dr. Schaefer

Keywords

diagnostic challenges, small vessel vasculitis, iga monoclonal gammopathy, leukocytoclastic vasculitis, erythema elevatum diutinum (eed)

Abstract

Erythema Elevatum Diutinum (EED) is a distinctive form of chronic leukocytoclastic vasculitis characterized by red to brown papules, plaques, and nodules that favor the extensor aspect of the extremities. EED is a benign condition but may be associated with several systemic diseases, including hematologic disorders, infections, and autoimmune conditions. EED is a rare entity of vasculitis, with less than 400 cases being reported in world literature to date. We present a rare case of a 61-year-old male with IgA monoclonal gammopathy of undetermined significance (MGUS) and a 17-year history of EED that improved significantly with dapsone treatment. 

References

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3. Patnala GP, Sunandini AP, Rayavarapu R, Yandapalli PS: Erythema elevatum diutinum in association with IgAmonoclonalgammopathy:Ararecasereport.IndianDermatolOnlineJ.2016,7:300-303. 10.4103/2229- 5178.185472

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