Atypical Fibroxanthoma of the External Ear: Case Report and Review of Literature

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Timothy Nyckowski
Roger Ceilley
Andrew Bean


atypical fibroxanthoma, ear, auricle


Atypical fibroxanthoma (AFX) is a rare, dermal- based mesenchymal neoplasm. Clinically, these tumors are characterized by rapid, exophytic growth and epidermal ulceration.1 Despite striking clinical features and growth pattern, it is considered to be a tumor of low- to intermediate- malignant potential.1-3. We report a case of an 89 year old Caucasian male that had a 1 month history of a rapidly enlarging, pedunculated neoplasm on the scapha of his right ear. Histologic and immunohistochemical analysis of the lesion were consistent with atypical fibroxanthoma. After a biopsy, the patient underwent a complete resection with Mohs micrographic surgery and remains asymptomatic 6 months later. This 3.0 x 2.0 cm lesion emerged over a 4-5 week period, representing the most rapid growing AFX of the external ear reported in the literature.


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